Tay-Sachs Disease Ganglioside
《英文msh詞典》Tay-Sachs Disease Ganglioside
[同義詞] Tay-Sachs Disease Ganglioside
[主題詞] G(M2) Ganglioside
[中文釋義] 泰-薩克斯病神經節苷脂
[英文釋義] A glycosphingolipid that accumulates due to a deficiency of hexosaminidase A or B (BETA-N-ACETYLHEXOSAMINIDASE),or GM2 activator protein,resulting in GANGLIOSIDOSES,heredity metabolic disorders that include TAY-SACHS DISEASE and SANDHOFF DISEASE.